UNUSUAL CARDIAC ANOMALY.

An Unusual Cardiac Anomaly: Ebstein-like Malformation

E BSTEIN’S ANOMALY, FIRST DESCRIBED in 1866, is relatively rare. It is a downward displacement of the tricuspid (right atrioventricular) valve below its annulus, dividing the right heart into a relatively large atrium and a small, at times functionless, right ventricle. The foramen ovale is usually patent and there may be other intracardiac anomalies.” We are describing a similar lesion involvi...

Cardiac arrest in an adolescent with Uhl’s anomaly: Two unusual cardiac arrhythmia mechanisms

Introduction Uhl’s disease is a rare congenital cardiac anomaly characterized by partial or complete absence of the right ventricular free wall myocardium, which is replaced by fibroelastic and adipose tissue. Complications that result can be divided into either right ventricular dysfunction with congestive heart failure, or arrhythmias. While ventricular arrhythmias predominate, there are case...

Digeorge syndrome presenting with uncommon cardiac anomaly and hepatomegaly

Digeorge syndrome is caused by microdeletion of a large region of chromosome 22q11.2 lead to the abnormal development of the third and fourth pharyngeal pouches. This syndrome is characterized by hypoparathyroidism, cellular immune deficiency secondary to thymic hypoplasia, congenital heart disease and dysmorphic facial features. In this case report, we describe a 4month old boy who presented w...

Unusual electrocardiographic changes in Ebstein's anomaly.

Unusual congenital coronary anomaly and myocardial ischaemia.

Angiography was used to diagnose a rare congenital coronary anomaly with myocardial ischaemia in a woman with typical angina. All three coronary arteries arose from a solitary coronary ostium in the right aortic sinus; the left anterior descending coronary artery followed a septal course, the circumflex coronary artery ran behind the ascending aorta, and the right coronary artery followed a nor...